Caroli disease, also known as Caroli syndrome or congenital hepatic fibrosis, is a rare genetic condition that affects the liver and bile ducts. The condition is characterized by the enlargement and dilation of the intrahepatic bile ducts, resulting in liver complications. Although there are no specific synonyms for Caroli disease, it is commonly referred to as Caroli syndrome or congenital hepatic fibrosis, which describe the primary aspects of the condition. These synonyms allow for better communication and understanding among medical professionals, facilitating research, diagnosis, and treatment options for individuals affected by this challenging liver disorder.