Incontinentia Pigmenti is a rare genetic disorder that affects the skin, hair, nails, teeth, and nervous system. There are many synonyms for this condition, including Bloch-Sulzberger syndrome, Bloch-Siemens syndrome, Melanoblastosis cutis, and Pigmentary incontinence. Incontinentia Pigmenti is a progressive disorder that usually appears in infants and young children. It is characterized by skin lesions that can range from blisters to hyperpigmentation. The condition can also cause dental abnormalities, developmental delays, and vision problems. Despite its many synonyms, the condition known as Incontinentia Pigmenti is still relatively unknown, and more research is needed to better understand its causes and potential treatments.