Long QT Syndrome is a genetic heart disorder characterized by a prolonged QT interval on an electrocardiogram. There are several synonyms used when referring to this condition, including LQTS, Romano-Ward Syndrome, and Jervell and Lange-Nielsen Syndrome. Romano-Ward Syndrome is the most common form of Long QT Syndrome, which results from a mutation in a single gene. Jervell and Lange-Nielsen Syndrome, on the other hand, is a rare variant of LQTS that is inherited in an autosomal recessive pattern. Regardless of the terminology used, Long QT Syndrome can lead to a range of cardiac events, including arrhythmias, syncope, and sudden cardiac death. Early diagnosis and management are essential in preventing adverse outcomes.