There are many synonyms for the term "PAVR", which stands for "Pulmonary Atresia with Ventricular Septal Defect and Right Ventricular Hypoplasia". This condition is a rare congenital heart defect that affects the pulmonary valve, the ventricular septum, and the right ventricle of the heart. Some of the synonyms for PAVR include Tetralogy of Fallot with pulmonary atresia, Unifocalization of Major Aortopulmonary Collateral Arteries (MAPCAs), and Critical Pulmonary Stenosis with Intact Ventricular Septum. These terms are often used interchangeably in medical literature to describe similar heart defects that share similar features and require similar treatment options. Early diagnosis and prompt medical intervention are crucial for the successful management of PAVR and related conditions.